Supratentorial haemangioblastoma not associated with Von Hippel Lindau complex or polycythaemia: case report and literature review.
Solitary or multiple supratentorial haemangioblastomas are rare and may be associated with Von Hippel-Lindau complex (VHLC), polycythaemia or a family history of VHLC. An extensive review of the literature (1902-1992) has revealed 112 cases. They account for 2-8% of all haemangioblastomas and are commonly intraparenchymatous (86.8%) and infrequently intraventricular (6.6%). However, a meningeal location (5.6%) is extremely rare. Only one case of a solitary leptomeningeal haemangioblastoma has previously been reported and this was associated with a family and personal history of VHLC, cerebellar haemangioblastomas and renal carcinoma. We report a solitary solid left parietal leptomeningeal haemangioblastoma mimicking a meningioma or a secondary deposit on computed tomography in a 72-year-old male. There were no manifestations of or a family history of VHLC or polycythaemia.
a Departments of Surgical Neurology and Pathology, Morriston Hospital, Morriston, Swansea SA66NL, Wales.
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R Sharma I P Cast C O'Brien
Cerebral;Computed Tomography;Haemangioblastoma;Leptomeninges;Prognosis;Solitary;Supratentorial