Evisceration in patients with Sturge-Weber syndrome.
The management of blind, painful eyes in Sturge-Weber syndrome patients poses unique challenges to the oculoplastic surgeon. Intraocular and orbital vascular malformations and calcification may theoretically lead to unexpected hemorrhage and difficulty placing an implant in a calcified scleral shell. We present two cases of patients with Sturge-Weber syndrome with blind, painful eyes who underwent evisceration with silicone implant and discuss the relevant current literature. Both of our patients had uncomplicated surgeries and post-operative courses. Our literature review reveals that both evisceration and enucleation are viable surgical options for globe removal in Sturge-Weber syndrome, yet careful preoperative planning must be undertaken to minimize risk.
a Ruiz Department of Ophthalmology and Visual Science , The University of Texas Health Science Center at Houston , Houston , Texas , USA.
Helen
H
Merritt
a Ruiz Department of Ophthalmology and Visual Science , The University of Texas Health Science Center at Houston , Houston , Texas , USA.
Margaret L
ML
Pfeiffer
a Ruiz Department of Ophthalmology and Visual Science , The University of Texas Health Science Center at Houston , Houston , Texas , USA.|b Robert Cizik Eye Clinic , Houston , Texas , USA.
Margaret E
ME
Phillips
a Ruiz Department of Ophthalmology and Visual Science , The University of Texas Health Science Center at Houston , Houston , Texas , USA.|b Robert Cizik Eye Clinic , Houston , Texas , USA.
Karina
K
Richani
D001766:Blindness / Q000601:surgery; D017234:Eye Evisceration; D058447:Eye Pain / Q000601:surgery; D005137:Eye, Artificial; D006801:Humans; D008297:Male; D008875:Middle Aged; D020273:Orbital Implants; D019919:Prosthesis Implantation; D013341:Sturge-Weber Syndrome / Q000175:diagnosis / Q000601:surgery*
Choroidal hemangioma enucleation; Sturge–Weber syndrome; evisceration