Perioperative considerations in infantile neuroaxonal dystrophy.
Infantile neuroaxonal dystrophy is a rare neurological disorder that is universally fatal with life expectancy under 10 years. A 10-year-old boy with infantile neuroaxonal dystrophy and severe neuromuscular scoliosis underwent posterior spinal fusion following halo traction. He was successfully extubated to bilevel positive airway pressure on postoperative day 3 and discharged home on postoperative day 11. Infantile neuroaxonal dystrophy presents several perioperative challenges including concerns for difficult intubation and respiratory dysfunction.
Department of Anesthesiology, Perioperative and Pain Medicine, Boston Children's Hospital, Boston, MA, USA.
Jina L
JL
Sinskey
Department of Anesthesiology, Perioperative and Pain Medicine, Boston Children's Hospital, Boston, MA, USA.
Robert S
RS
Holzman
D002648:Child; D006801:Humans; D008297:Male; D019150:Neuroaxonal Dystrophies / Q000601:surgery*; D019990:Perioperative Care / Q000379:methods*; D013123:Spinal Fusion / Q000379:methods*; D016896:Treatment Outcome
general anesthesia; neuroaxonal dystrophies; neurodegenerative diseases; scoliosis