An unusual thoracic localizations of Erdheim- Chester disease: A case report.
Erdheim- Chester disease is a rare non- Langerhans cell histiocytosis that usually involves the bones, heart, central nervous system, retroperitoneum, eyes, kidneys, skin and adrenals. Lungs are affected in up to one-half cases; at CT scan various patterns are described: interstitial disease, consolidations, micronodules and microcysts, with or without pleural involvement. We presented a case of a 59 year-old man with unusual intrathoracic manifestation of Erdheim- Chester disease. Singularities of our report are the lonely thoracic involvement at the onset of the disease and a histiocytic lesion in the posterior mediastinum.
Pulmonary Unit, "C. e G. Mazzoni" Hospital, Ascoli Piceno, Italy.
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Massaccesi
Pulmonary Unit, "C. e G. Mazzoni" Hospital, Ascoli Piceno, Italy.
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Colella
Pulmonary Unit, "C. e G. Mazzoni" Hospital, Ascoli Piceno, Italy.
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Fioretti
Pulmonary Unit, "C. e G. Mazzoni" Hospital, Ascoli Piceno, Italy.
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D'Emilio
Pulmonary Unit, "C. e G. Mazzoni" Hospital, Ascoli Piceno, Italy.
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Panella
Pulmonary Unit, "C. e G. Mazzoni" Hospital, Ascoli Piceno, Italy.
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Primomo
Department of Pathology, "Ospedali Riuniti", Ancona, Italy.
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Barbisan
Pulmonary Unit, "C. e G. Mazzoni" Hospital, Ascoli Piceno, Italy.
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Pela
Department of Diseases of the Thorax, GB Morgagni Hospital, Forlì, Italy; Department of Respiratory Diseases and Allergy, Aarhus University Hospital, Aarhus, Denmark.
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Poletti