Atypical Teratoid/Rhabdoid Tumor of the Sellar Region in an Adult With Long Survival: Case Report and Review of the Literature.
Atypical teratoid/rhabdoid tumor (AT/RT) is a highly malignant central nervous system neoplasm usually diagnosed in young children, although it can occur in adults. Prognosis for AT/RT is poor, with a median survival of 10 - 11 months. We report a rare case of adult sellar and suprasellar AT/RT in a 36-year-old female patient. She was treated with multi-modalities including surgery, chemotherapy and radiation. She markedly improved following treatment with no recurrence in 3 years follow-up. To our knowledge, this is the 11th case of an adult-onset AT/RT in the sellar or suprasellar region with favorable long-term outcome.
Obesity, Endocrine, and Metabolism Center, King Fahad Medical City, Riyadh, Saudi Arabia; King Fahad Medical City, College of Medicine, King Saud bin Abdulaziz University for Health Science, Riyadh, Saudi Arabia.
Mussa Hussain
MH
Almalki
Obesity, Endocrine, and Metabolism Center, King Fahad Medical City, Riyadh, Saudi Arabia.
Ashjan
A
Alrogi
Department of Neurosurgery, National Neuroscience Institute, King Fahad Medical City, Riyadh, Saudi Arabia.
Abdulkarim
A
Al-Rabie
King Fahad Medical City, College of Medicine, King Saud bin Abdulaziz University for Health Science, Riyadh, Saudi Arabia; Department of Anatomical Pathology, King Fahad Medical City, Riyadh, Saudi Arabia.
Sadeq
S
Al-Dandan
Oncology Center, King Fahad Medical City, Riyadh, Saudi Arabia.
Abdullah
A
Altwairgi
Department of Neurosurgery, National Neuroscience Institute, King Fahad Medical City, Riyadh, Saudi Arabia.
Yasser
Y
Orz
Atypical teratoid/rhabdoid tumor; Chemotherapy; Radiotherapy; Sellar/suprasellar lesion; Surgery