Mounier-Kuhn syndrome: a case of tracheal smooth muscle remodeling.
Mounier-Kuhn syndrome is a rare clinical disorder characterized by tracheobronchial dilation and recurrent lower respiratory tract infections. While the etiology of the disease remains unknown, histopathological analysis of Mounier-Kuhn airways demonstrates that the disease is, in part, characterized by cellular changes in airway smooth muscle.
Department of Internal Medicine University of Iowa Iowa City Iowa USA; Department of Molecular Physiology and Biophysics University of Iowa Iowa City Iowa USA.
Daniel P
DP
Cook
Department of Internal Medicine University of Iowa Iowa City Iowa USA; Department of Biomedical Engineering University of Iowa Iowa City Iowa USA.
Ryan J
RJ
Adam
Department of Internal Medicine University of Iowa Iowa City Iowa USA.
Mahmoud H
MH
Abou Alaiwa
Department of Internal Medicine University of Iowa Iowa City Iowa USA.
Michael
M
Eberlein
Department of Internal Medicine University of Iowa Iowa City Iowa USA.
Julia A
JA
Klesney-Tait
Department of Cardiothoracic Surgery University of Iowa Iowa City Iowa USA.
Kalpaj R
KR
Parekh
Department of Pathology University of Iowa Iowa City Iowa USA.
David K
DK
Meyerholz
Department of Internal Medicine University of Iowa Iowa City Iowa USA; Department of Molecular Physiology and Biophysics University of Iowa Iowa City Iowa USA; Department of Biomedical Engineering University of Iowa Iowa City Iowa USA; Pappajohn Biomedical Institute University of Iowa Iowa City Iowa USA.
David A
0000-0003-0893-9015
DA
Stoltz
Airway remodeling; Mounier–Kuhn syndrome; airway smooth muscle; tracheobronchomalacia