[Pulmonary Langerhans' cell histiocytosis (PLCH) revealed by pneumothorax: about a case].
Langerhans cell histiocytosis is a rare disease of unknown etiology characterized by the infiltration of Langerhans cells in one or more organs. It has a polymorphic clinical presentation. We report the case of Mr R.Y, age 22, with 8 pack year history of smoking, admitted to hospital with complete spontaneous right-sided pneumothorax. Chest drainage was performed with good evolution. Control chest CT scan showed multiple diffuse cyst formations, predominant in the upper lobes. Lab and imaging tests were performed in order to detect systemic histiocytosis with negative results. Patient's evolution was marked by pneumothorax recurrence; pleurodesis and lung biopsy were performed which confirmed the diagnosis. The diagnosis of Langerhans cell histiocytosis should be evoked in front of pneumothorax associated with lung cystic. The diagnosis is easy in front of a suggestive clinical and radiological picture. Nevertheless, therapeutic options are limited and pneumothorax recurrence is common.
Service de Pneumologie, Hôpital Arrazi, CHU Mohamed VI, Laboratoire PCIM, UCAM, Marrakech, Maroc.
Hafsa
H
Sajiai
Service de Pneumologie, Hôpital Arrazi, CHU Mohamed VI, Laboratoire PCIM, UCAM, Marrakech, Maroc.
Mariam
M
Rachidi
Service de Pneumologie, Hôpital Arrazi, CHU Mohamed VI, Laboratoire PCIM, UCAM, Marrakech, Maroc.
Hind
H
Serhane
Service de Pneumologie, Hôpital Arrazi, CHU Mohamed VI, Laboratoire PCIM, UCAM, Marrakech, Maroc.
Salma
S
Aitbatahar
Service de Pneumologie, Hôpital Arrazi, CHU Mohamed VI, Laboratoire PCIM, UCAM, Marrakech, Maroc.
Lamyae
L
Amro
D001706:Biopsy; D006646:Histiocytosis, Langerhans-Cell / Q000175:diagnosis* / Q000473:pathology; D006801:Humans; D008297:Male; D018700:Pleurodesis / Q000379:methods*; D011030:Pneumothorax / Q000209:etiology* / Q000628:therapy; D012008:Recurrence; D014057:Tomography, X-Ray Computed; D055815:Young Adult
Histiocytosis; cyst; pneumothorax