Prophylactic Pulmonary Artery Reduction in a Young Female with Severe Pulmonary Hypertension from Complete Atrioventricular Septal Defect.
Management of severely dilated pulmonary artery (PA) associated with severe pulmonary hypertension from congenital heart disease remains controversial, primarily due to its rare nature and concern for perioperative unpredictable complications. Herein, we report a 25 year-old female with a severely dilated PA (up to 73 mm), who was successfully treated by a PA graft replacement by creating a Y-shaped conduit using a 28 mm hemashield tube in the main PA and a 20 mm hemashield tube in both proximal parts of the branch PA.
Department of Pediatrics, Seoul National University Children's Hospital, Seoul, Korea.
Sun Hyang
SH
Lee
Department of Pediatrics, Seoul National University Children's Hospital, Seoul, Korea.
Bo Sang
BS
Kwon
Department of Pediatrics, Seoul National University Children's Hospital, Seoul, Korea.
Gi Beom
GB
Kim
Department of Pediatrics, Seoul National University Children's Hospital, Seoul, Korea.
Eun Jung
EJ
Bae
Department of Pediatrics, Seoul National University Children's Hospital, Seoul, Korea.
Chung Il
CI
Noh
Department of Thoracic and Cardiovascular Surgery, Seoul National University Children's Hospital, Seoul, Korea.
Woong Han
WH
Kim
Congenital heart defects; Pulmonary arterial hypertension; Pulmonary surgical procedure