title: Uterine conserving surgery in a case of cervicovaginal agenesis with unicornuate uterus.
abstract: The presence of cervicovaginal agenesis with unicornuate uterus is a very rare mullerian anomaly. Its true incidence is still unknown. The presence of functioning unicornuate uterus poses a great challenge for a gynecologist because a successful repair could restore normal menses and may preserve a patient's fertility. Hence, we report a case of 16-year-old unmarried female who presented with chief complaints of primary amenorrhea with cyclical lower abdominal pain. On clinical and radiological evaluation, she was diagnosed with complete cervicovaginal agenesis with right unicornuate uterus (hematometra and hematosalpinx). She underwent vaginoplasty (McIndoes method) along with uterovaginal anastomosis by neocervix formation, in order to preserve her uterus. On follow-up, her vagina was completely healed, and she was menstruating normally.
authors.affiliation: Department of Obstetrics and Gynecology, Institute of Kidney Diseases and Research Centre, Institute of Transplantation Sciences, B. J. Medical College, Bikaner, Rajasthan, India.
authors.forename: Vineet
authors.initials: V
authors.lastname: Mishra
authors.affiliation: Department of Obstetrics and Gynecology, S. P. Medical College, Bikaner, Rajasthan, India.
authors.forename: Suwa Ram
authors.initials: SR
authors.lastname: Saini
authors.affiliation: Department of Obstetrics and Gynecology, Institute of Transplantation Sciences, Ahmedabad, Gujarat, India.
authors.forename: Sakshi
authors.initials: S
authors.lastname: Nanda
authors.affiliation: Department of Obstetrics and Gynecology, Institute of Transplantation Sciences, Ahmedabad, Gujarat, India.
authors.forename: Sumesh
authors.initials: S
authors.lastname: Choudhary
authors.affiliation: Clinical Fellow, Institute of Kidney Diseases and Research Centre, Institute of Transplantation Sciences, Ahmedabad, Gujarat, India.
authors.forename: Priyankur
authors.initials: P
authors.lastname: Roy
authors.affiliation: Department of Obstetrics and Gynecology, Institute of Transplantation Sciences, Ahmedabad, Gujarat, India.
authors.forename: Tanvir
authors.initials: T
authors.lastname: Singh
keywords: Hematometra; hematosalpinx; vaginal agenesis; vaginoplasty