title: Anesthetic Management in a Child With Niemann-Pick Disease.
abstract: Niemann-Pick is a lipid storage disease that results from a lysosomal enzyme deficiency (sphingomyelinase). It has different presentations, and it may affect various organs such as the central nervous system, kidney, liver, and spleen. Due to the complexity of the disease, careful perianesthetic management is necessary in order to reduce the risks and sequels. As there is little evidence available in the literature regarding the anesthetic implications of such patients, in this case report we describe the anesthetic management of a two-year-old female with Niemann-Pick disease.
authors.affiliation: Anesthesiology and Critical Care, Tehran University of Medical Sciences, Tehran, IR Iran.
authors.forename: Ebrahim
authors.initials: E
authors.lastname: Espahbodi
authors.affiliation: Anesthesiology and Critical Care, Tehran University of Medical Sciences, Tehran, IR Iran.
authors.forename: Amir Abbas
authors.initials: AA
authors.lastname: Yaghooti
authors.affiliation: Anesthesiology and Critical Care, Tehran University of Medical Sciences, Tehran, IR Iran.
authors.forename: Abbas
authors.initials: A
authors.lastname: Ostadalipour
authors.affiliation: Anesthesiology and Critical Care, Tehran University of Medical Sciences, Tehran, IR Iran.
authors.forename: Shaqayeq
authors.initials: S
authors.lastname: Marashi
keywords: Anesthesia; Child; Niemann-Pick