title: Ascending aortic aneurysm and diaphragmatic hernia in a case of Marfan syndrome.
abstract: Marfan syndrome commonly affects the skeletal, ocular, and cardiovascular systems. Involvement of the gastrointestinal system is known but uncommon. Intervention depends upon the system involved and the severity of symptoms. Special awareness is required for the diagnosis and management of gastrointestinal involvement in these patients. We report a rare case of simultaneous surgical repair of an ascending aortic aneurysm and a type IV hiatal hernia in a 35-year-old man with Marfan syndrome.
authors.affiliation: UN Mehta Institute of Cardiology and Research Center (affiliated to BJ Medical College), Ahmedabad, India.
authors.forename: Jignesh
authors.initials: J
authors.lastname: Kothari
authors.affiliation: UN Mehta Institute of Cardiology and Research Center (affiliated to BJ Medical College), Ahmedabad, India.
authors.forename: Manish
authors.initials: M
authors.lastname: Hinduja
authors.affiliation: UN Mehta Institute of Cardiology and Research Center (affiliated to BJ Medical College), Ahmedabad, India.
authors.forename: Kinnaresh
authors.initials: K
authors.lastname: Baria
authors.affiliation: UN Mehta Institute of Cardiology and Research Center (affiliated to BJ Medical College), Ahmedabad, India.
authors.forename: Himani
authors.initials: H
authors.lastname: Pandya
mesh_terms: D000328:Adult; D001014:Aortic Aneurysm / Q000000981:diagnostic imaging / Q000209:etiology* / Q000601:surgery; D001027:Aortography / Q000379:methods; D019917:Blood Vessel Prosthesis Implantation; D000072226:Computed Tomography Angiography; D006551:Hernia, Hiatal / Q000000981:diagnostic imaging / Q000209:etiology* / Q000601:surgery; D059685:Herniorrhaphy; D006801:Humans; D008297:Male; D008382:Marfan Syndrome / Q000150:complications* / Q000175:diagnosis; D016896:Treatment Outcome
keywords: Aortic aneurysm; Hernia; Marfan syndrome; diaphragmatic