title: Isolated Hypoplasia of Left Pulmonary Artery with Agenesis of Left Lobe of Thyroid: A Case Report.
abstract: Isolated Unilateral hypoplasia or agenesis of a branch of pulmonary artery is very rare. It is usually seen associated with congenital heart diseases such as tetralogy of Fallot, atrial septal defect, coarctation of the aorta, right aortic arch, truncus arteriosus, patent ductus arteriosus and pulmonary atresia. It occurs as a result of lack of embryological development of either the left or right sixth aortic arch and has been found to present itself with various clinical manifestations as during childhood it presents as contralateral pulmonary hypertension and in adults as haemoptysis. Early diagnosis and early surgical indication avoids the evolution of pulmonary hypertension to unfavourble state of more severe and progressive degrees and also prevents the development of pulmonary systemic collateral circulation, which is mainly responsible for subsequent haemoptysis in the adulthood. We hereby, report the case of an infant who presented with features of lower respiratory tract infection and later diagnosed as isolated congenital hypoplasia of left pulmonary artery and hence planned for proper follow-up for early surgery thereby preventing complications in the future.
authors.affiliation: Registrar, Department of Cardiology, Chettinad Hospital and Research Institute , Chennai, Tamil Nadu, India .
authors.forename: Mohammed Abdul
authors.initials: MA
authors.lastname: Khadir
authors.affiliation: Associate Professor, Department of Cardiology, Chettinad Hospital and Research Institute , Chennai, Tamil Nadu, India .
authors.forename: Ganesh
authors.initials: G
authors.lastname: Narayana
authors.affiliation: Assistant Professor, Department of Paediatrics, Chettinad Hospital and Research Institute , Chennai, Tamil Nadu, India .
authors.forename: Ganavi
authors.initials: G
authors.lastname: Ramagopal
authors.affiliation: Professor and Head, Department of Cardiology, Chettinad Hospital and Research Institute , Chennai, Tamil Nadu, India .
authors.forename: Pradeep G
authors.initials: PG
authors.lastname: Nayar
keywords: Hypoplasic lung; Hypoxia; Pulmonary hypertension; Respiratory distress