title: Pericardio-Amniotic Shunting for Incomplete Pentalogy of Cantrell.
abstract: A 27-year-old woman, gravida 2, para 0, presented with an incomplete Pentalogy of Cantrell with an omphalocele, diaphragmatic hernia, and a pericardial defect at 32 weeks' gestation. A large pericardial effusion compressed the lungs and had led to a reduced lung growth with an observed-to-expected total lung volume of 28% as measured by MRI. The effusion disappeared completely after the insertion of a pericardio-amniotic shunt at 33 weeks. After birth, the newborn showed no signs of pulmonary hypoplasia and underwent a surgical correction of the defect. Protracted wound healing and a difficult withdrawal from opioids complicated the neonatal period. The child was discharged on postnatal day 105 in good condition. This case demonstrates that in case of Pentalogy of Cantrell with large pericardial effusion, the perinatal outcome might be improved by pericardio-amniotic shunting.
authors.affiliation: Department of Development and Regeneration, Organ Systems, KU Leuven, Leuven, Belgium.
authors.forename: Alexander C
authors.initials: AC
authors.lastname: Engels
authors.forename: Anne
authors.initials: A
authors.lastname: Debeer
authors.forename: Francesca M
authors.initials: FM
authors.lastname: Russo
authors.forename: Michael
authors.initials: M
authors.lastname: Aertsen
authors.forename: Katleen
authors.initials: K
authors.lastname: Aerts
authors.forename: Marc
authors.initials: M
authors.lastname: Miserez
authors.forename: Jan
authors.initials: J
authors.lastname: Deprest
authors.forename: Liesbeth
authors.initials: L
authors.lastname: Lewi
authors.forename: Roland
authors.initials: R
authors.lastname: Devlieger
mesh_terms: D000328:Adult; D000714:Anastomosis, Surgical / Q000379:methods*; D005260:Female; D006554:Hernia, Umbilical / Q000000981:diagnostic imaging / Q000601:surgery*; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008279:Magnetic Resonance Imaging; D008297:Male; D058502:Pentalogy of Cantrell / Q000000981:diagnostic imaging / Q000601:surgery*; D010490:Pericardial Effusion / Q000000981:diagnostic imaging / Q000601:surgery*; D010496:Pericardium / Q000000981:diagnostic imaging / Q000601:surgery*; D011247:Pregnancy; D016896:Treatment Outcome; D016216:Ultrasonography, Prenatal