title: [Epidemiological trends of cystic fibrosis in France: 10-year perspective].
abstract: Cystic fibrosis (CF) is the most prevalent severe genetic disease in the Caucasian population. It affects approximately 7000 patients in France, of whom 54% are adults (≥18 years old). Improvement in therapeutic management has resulted in a major decrease in pediatric mortality and an increase in the longevity of adults with CF, resulting in a major increase in the number of adult patients over the past 20 years. Demographic forecasts indicate that the French adult CF population will increase by approximately 2000 patients between 2010 and 2025. These data indicate the need for an adaptation of the healthcare system for providing high quality care to all CF patients in the near future.
authors.affiliation: Service de Pneumologie et Centre de Mucoviscidose de l'adulte; Hôpital Cochin, Assistance Publique Hôpitaux de Paris, 75014 Paris, France; Université Paris Descartes, Sorbonne Paris Cité, Paris, France. Electronic address: pierre-regis.burgel@aphp.fr.
authors.forename: P-R
authors.initials: PR
authors.lastname: Burgel
mesh_terms: D015331:Cohort Studies; D003550:Cystic Fibrosis / Q000453:epidemiology* / Q000401:mortality / Q000628:therapy; D005602:France / Q000453:epidemiology; D006297:Health Services Accessibility / Q000639:trends; D006301:Health Services Needs and Demand / Q000639:trends; D006801:Humans; D033183:Interdisciplinary Communication; D000070516:Intersectoral Collaboration; D008017:Life Expectancy; D016040:Lung Transplantation / Q000639:trends