title: Challenging mitral valve repair for double-orifice mitral valve with noncompaction of left ventricular myocardium.
abstract: Double-orifice mitral valve (DOMV) is a relatively rare cardiac anomaly. Although usually associated with various cardiac anomalies, co-presence of DOMV and noncompaction of left ventricular myocardium (NCLVM) is extremely rare. Here, we present a 24-year-old male who underwent mitral valve repair using artificial chordae and annuloplasty at the posterior commissure for severe mitral regurgitation (MR), resulting from flail anterior leaflet of the larger postero-medial orifice and dilatation of left ventricle with NCLVM. One year later, he underwent second mitral valve repair for recurrence of MR. Further endoscopic evaluation of the left ventricle, and reinforcement via artificial ring, enabled us to achieve repair.
authors.affiliation: Department of Cardiovascular Surgery, St. Luke's International Hospital, 9-1 Akashicho, Chuoku, Tokyo, 104-8560, Japan. manayama@luke.ac.jp.
authors.forename: Manabu
authors.initials: M
authors.lastname: Yamasaki
authors.affiliation: Department of Cardiovascular Surgery, St. Luke's International Hospital, 9-1 Akashicho, Chuoku, Tokyo, 104-8560, Japan.
authors.forename: Hiroyasu
authors.initials: H
authors.lastname: Misumi
authors.affiliation: Department of Cardiovascular Surgery, St. Luke's International Hospital, 9-1 Akashicho, Chuoku, Tokyo, 104-8560, Japan.
authors.forename: Kohei
authors.initials: K
authors.lastname: Abe
authors.affiliation: Department of Cardiovascular Surgery, St. Luke's International Hospital, 9-1 Akashicho, Chuoku, Tokyo, 104-8560, Japan.
authors.forename: Kohei
authors.initials: K
authors.lastname: Kawazoe
mesh_terms: D000015:Abnormalities, Multiple; D058385:Cardiac Valve Annuloplasty / Q000379:methods*; D019560:Echocardiography, Three-Dimensional; D005500:Follow-Up Studies; D006330:Heart Defects, Congenital / Q000175:diagnosis / Q000601:surgery*; D006801:Humans; D008297:Male; D008943:Mitral Valve / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000601:surgery; D008944:Mitral Valve Insufficiency / Q000151:congenital / Q000175:diagnosis / Q000601:surgery*; D055815:Young Adult
keywords: Double orifice; Mitral regurgitation; Mitral valve repair