title: Isolated Pericardial Infiltration Without Myocardial Involvement in Light-Chain-Related Amyloidosis.
abstract: Light-chain-related amyloidosis is a systemic disease characterized by continuous accumulation of insoluble fibrillar proteins in different organs. Cardiac involvement is frequent in this condition. However, atypical presentations and unusual amyloid deposits localization may be encountered making the diagnosis challenging. We present here a case of a light-chain-related pericardial amyloidosis without evidence of myocardial involvement and emphasize the difficulty and importance of amyloidosis typing before starting treatment.
authors.affiliation: Department of Internal Medicine, Tenon Hospital, Pierre et Marie Curie University, Paris, France.
authors.forename: Sophie
authors.initials: S
authors.lastname: Georgin-Lavialle
authors.affiliation: University Paris-Est Créteil, Créteil, France; Mondor Amyloidosis Network, Créteil, France; Department of Cardiology, Henri-Mondor Teaching Hospital, Créteil, France; GRC Amyloid Research Institute, Créteil, France.
authors.forename: Aziz
authors.initials: A
authors.lastname: Guellich
authors.affiliation: University Paris-Est Créteil, Créteil, France; Mondor Amyloidosis Network, Créteil, France; GRC Amyloid Research Institute, Créteil, France; Department of Radiology, Henri-Mondor Teaching Hospital, Créteil, France.
authors.forename: Jean-François
authors.initials: JF
authors.lastname: Deux
authors.affiliation: Department of Pathology, Tenon Hospital, Paris, France.
authors.forename: David
authors.initials: D
authors.lastname: Buob
authors.affiliation: University Paris-Est Créteil, Créteil, France; Mondor Amyloidosis Network, Créteil, France; Department of Cardiology, Henri-Mondor Teaching Hospital, Créteil, France; GRC Amyloid Research Institute, Créteil, France. Electronic address: thibaud.damy@hmn.aphp.fr.
authors.forename: Thibaud
authors.initials: T
authors.lastname: Damy
mesh_terms: D000686:Amyloidosis / Q000150:complications* / Q000000981:diagnostic imaging; D006801:Humans; D007147:Immunoglobulin Light Chains / Q000502:physiology*; D008297:Male; D008875:Middle Aged; D010490:Pericardial Effusion / Q000209:etiology*; D014057:Tomography, X-Ray Computed
chemical_list: D007147:Immunoglobulin Light Chains