title: Modified Cone Reconstruction of the Tricuspid Valve for Ebstein Anomaly as Performed in Siberia.
abstract: The cone reconstruction technique, first described by da Silva and modified by Dearani and by others, has become the repair method of choice in patients with Ebstein anomaly of the tricuspid valve. This report details the outcome of the modified cone reconstruction technique in 6 children who underwent surgical correction of Ebstein anomaly at the Tomsk Institute of Cardiology in Siberia. From 2012 through 2015, 4 boys and 2 girls (age range, 11 mo-12 yr) underwent surgery to correct Ebstein anomaly. All had presented with cyanosis, exertional dyspnea, fatigue, or new-onset atrial arrhythmia, and none had undergone previous cardiac surgery. All survived the operation. One patient needed tricuspid valve replacement with a bioprosthesis after early breakdown of the cone reconstruction. As of December 2016, all the patients had no symptoms, tricuspid stenosis, or arrhythmia. This series indicates that cone reconstruction-the most anatomic repair technique for the dysmorphic Ebstein tricuspid valve-can be successfully performed in pediatric heart centers with a large experience.
authors.forename: Evgeny V
authors.initials: EV
authors.lastname: Krivoshchekov
authors.forename: Jaeger P
authors.initials: JP
authors.lastname: Ackerman
authors.forename: Olga S
authors.initials: OS
authors.lastname: Yanulevich
authors.forename: Alexander A
authors.initials: AA
authors.lastname: Sokolov
authors.forename: Nadezhda V
authors.initials: NV
authors.lastname: Ershova
authors.forename: Joseph A
authors.initials: JA
authors.lastname: Dearani
authors.forename: Frank
authors.initials: F
authors.lastname: Cetta
mesh_terms: D006348:Cardiac Surgical Procedures / Q000009:adverse effects / Q000379:methods*; D002648:Child; D002675:Child, Preschool; D004437:Ebstein Anomaly / Q000000981:diagnostic imaging / Q000503:physiopathology / Q000601:surgery*; D018618:Echocardiography, Doppler, Color; D005260:Female; D006801:Humans; D007223:Infant; D008297:Male; D019651:Plastic Surgery Procedures / Q000009:adverse effects; D020127:Recovery of Function; D012800:Siberia; D016896:Treatment Outcome; D014261:Tricuspid Valve / Q000002:abnormalities / Q000000981:diagnostic imaging / Q000503:physiopathology / Q000601:surgery*
keywords: Cardiac surgical procedures/methods; Ebstein anomaly/surgery; reconstructive surgical procedures/methods; recovery of function; reproducibility of results; treatment outcome; tricuspid valve insufficiency/etiology/surgery; tricuspid valve/abnormalities/surgery