title: Congenital Orbital Teratoma.
abstract: We report a case of congenital orbital teratoma. A 3-day-old male, born at 39 weeks' gestation without relevant prenatal history, presented with a large vascularized proptotic mass distorting the left midface. Laboratory studies showed elevated serum alpha-fetoprotein (12,910 ng/ml). Computed tomography showed a multiloculated heterogeneous lesion composed of hypodense and hyperdense calcified areas encompassing the whole orbital cavity with expansion of the bony walls, as well as forward displacement and compression of the eyeball without extension to surrounding structures. Clinical, imaging and laboratory features were consistent with congenital orbital teratoma. Due to pronounced proptosis with exposure keratopathy and corneal perforation, no motility of the globe and no vision in the affected eye in a resource-limited setting, the patient underwent orbital exenteration. Histopathological examination confirmed the diagnosis of mature cystic teratoma. We describe the clinical course, radiographic and histopathological findings of this rare orbital tumor.
authors.affiliation: Ocular Diagnostic Unit, Clínica Oftalmológica de Santo Domingo, Santo Domingo, Dominican Republic; Universidad Iberoamericana (UNIBE) School of Medicine, Santo Domingo, Dominican Republic.
authors.forename: Fernando
authors.initials: F
authors.lastname: Pellerano
authors.affiliation: Department of Pediatric Ophthalmology, Hospital Infantil Dr. Robert Reid Cabral, Santo Domingo, Dominican Republic.
authors.forename: Elvis
authors.initials: E
authors.lastname: Guillermo
authors.affiliation: Department of Pediatric Ophthalmology, Hospital Infantil Dr. Robert Reid Cabral, Santo Domingo, Dominican Republic.
authors.forename: Gloreley
authors.initials: G
authors.lastname: Garrido
authors.affiliation: Department of Pathology, Hospital Infantil Dr. Robert Reid Cabral, Santo Domingo, Dominican Republic.
authors.forename: Pedro
authors.initials: P
authors.lastname: Berges
keywords: Congenital teratoma; Orbital tumor; Proptosis in a neonate