title: Kawasaki disease shock syndrome: a rare and severe complication of Kawasaki disease.
abstract: Kawasaki disease is an acute systemic vasculitis that occurs most commonly in young children. It affects medium-sized muscular arteries and the coronary arteries are the predominant site of involvement. Morbidity and mortality is generally due to coronary artery aneurysms that develop during the chronic phase. Although it is well known that Kawasaki disease can cause myocarditis, tachycardia and heart failure during acute stage, Kawasaki disease shock syndrome has been recently described. It is characterized by hypotension, signs and symptoms of poor perfusion and a shock-like state. Herein we describe two cases of Kawasaki disease shock syndrome that were treated in the pediatric intensive care unit and followed a course without morbidity or mortality.
authors.affiliation: Clinics of Pediatric Rheumatology, Kanuni Sultan Süleyman Research and Training Hospital, İstanbul, Turkey.
authors.forename: Mustafa
authors.initials: M
authors.lastname: Çakan
authors.affiliation: Clinics of Pediatrics, Kanuni Sultan Süleyman Research and Training Hospital, İstanbul, Turkey.
authors.forename: Hakan
authors.initials: H
authors.lastname: Gemici
authors.affiliation: Clinics of Pediatric Rheumatology, Kanuni Sultan Süleyman Research and Training Hospital, İstanbul, Turkey.
authors.forename: Nuray
authors.initials: N
authors.lastname: Aktay-Ayaz
authors.affiliation: Clinics of Pediatrics, Kanuni Sultan Süleyman Research and Training Hospital, İstanbul, Turkey.
authors.forename: Gonca
authors.initials: G
authors.lastname: Keskindemirci
authors.affiliation: Clinics of Pediatric Cardiology, Kanuni Sultan Süleyman Research and Training Hospital, İstanbul, Turkey.
authors.forename: Helen
authors.initials: H
authors.lastname: Bornaun
authors.affiliation: Clinic of Pediatrics, Acıbadem Maslak Hospital, İstanbul, Turkey.
authors.forename: Tarkan
authors.initials: T
authors.lastname: İkizoğlu
authors.affiliation: Division of Pediatric Cardiology, Department of Pediatrics, Koç University Faculty of Medicine, İstanbul, Turkey.
authors.forename: Alpay
authors.initials: A
authors.lastname: Çeliker
mesh_terms: D002648:Child; D002675:Child, Preschool; D005260:Female; D006801:Humans; D016756:Immunoglobulins, Intravenous / Q000627:therapeutic use*; D015278:Intensive Care Units, Pediatric; D008297:Male; D009080:Mucocutaneous Lymph Node Syndrome / Q000150:complications* / Q000175:diagnosis / Q000628:therapy; D012772:Shock, Septic / Q000209:etiology* / Q000628:therapy
chemical_list: D016756:Immunoglobulins, Intravenous
keywords: Kawasaki disease; Kawasaki disease shock syndrome; child; intensive care unit; toxic shock syndrome