title: Caesarean delivery in a pregnant woman with epidermolysis bullosa: anaesthetic challenges.
abstract: Epidermolysis bullosa is a heterogeneous group of hereditary diseases characterised by extreme fragility of skin and mucosa, with blister and lesion formation spontaneously or in response to trauma. Anaesthetic management of these patients is challenging with respect to positioning, monitoring, use of medical devices and airway management. These challenges are increased when managing labour. We report an elective caesarean delivery in a nulliparous woman with autosomal recessive dystrophic epidermolysis bullosa, managed successfully with spinal anaesthesia.
authors.affiliation: Centro Hospitalar do Porto, Largo Prof. Abel Salazar, Porto, Portugal. Electronic address: martaclaudiaaraujo@gmail.com.
authors.forename: M
authors.initials: M
authors.lastname: Araújo
authors.affiliation: Centro Hospitalar do Porto, Largo Prof. Abel Salazar, Porto, Portugal.
authors.forename: R
authors.initials: R
authors.lastname: Brás
authors.affiliation: Centro Hospitalar do Porto, Largo Prof. Abel Salazar, Porto, Portugal.
authors.forename: R
authors.initials: R
authors.lastname: Frada
authors.affiliation: Centro Hospitalar do Porto, Largo Prof. Abel Salazar, Porto, Portugal.
authors.forename: L
authors.initials: L
authors.lastname: Guedes-Martins
authors.affiliation: Centro Hospitalar do Porto, Largo Prof. Abel Salazar, Porto, Portugal.
authors.forename: P
authors.initials: P
authors.lastname: Lemos
mesh_terms: D000328:Adult; D000740:Anemia / Q000150:complications; D000773:Anesthesia, Obstetrical / Q000379:methods*; D001768:Blister / Q000473:pathology; D002585:Cesarean Section / Q000379:methods*; D016108:Epidermolysis Bullosa Dystrophica / Q000150:complications* / Q000473:pathology; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D009407:Nerve Block; D010149:Postoperative Pain / Q000188:drug therapy; D011247:Pregnancy; D011248:Pregnancy Complications; D012867:Skin / Q000473:pathology
keywords: Caesarean delivery; Epidermolysis bullosa; Regional anaesthesia