title: Cor triatriatum sinister with an intact interatrial septum and a decompressing vein in a toddler.
abstract: Cor triatriatum sinister is a very rare cardiac anomaly that may lead to pulmonary hypertension, right ventricular dilation, and eventually right heart failure. We report a case of a toddler who presented with respiratory distress and cardiomegaly and was found to have cor triatriatum sinister with a restrictive communication, decompressing vertical vein, pulmonary hypertension, severe tricuspid regurgitation, and severe right ventricular dysfunction. She underwent a successful surgical repair, with normalisation of right ventricular function and pulmonary artery pressure.
authors.affiliation: 1Division of Congenital Heart Surgery,Texas Children's Hospital,Houston,TX,United States of America.
authors.forename: Ziyad M
authors.initials: ZM
authors.lastname: Binsalamah
authors.affiliation: 1Division of Congenital Heart Surgery,Texas Children's Hospital,Houston,TX,United States of America.
authors.forename: Luis E
authors.initials: LE
authors.lastname: De León
authors.affiliation: 1Division of Congenital Heart Surgery,Texas Children's Hospital,Houston,TX,United States of America.
authors.forename: Jeffrey S
authors.initials: JS
authors.lastname: Heinle
mesh_terms: D054087:Atrial Septum / Q000000981:diagnostic imaging*; D006348:Cardiac Surgical Procedures / Q000379:methods*; D002675:Child, Preschool; D003310:Cor Triatriatum / Q000175:diagnosis* / Q000503:physiopathology / Q000601:surgery; D004452:Echocardiography; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D011669:Pulmonary Wedge Pressure / Q000502:physiology*; D014057:Tomography, X-Ray Computed; D016278:Ventricular Function, Right / Q000502:physiology*
keywords: Cor triatriatum; decompressing vertical vein; intact interatrial septum; persistent levoatrial cardinal vein; tricuspid regurgitation