title: Tricuspid Valve Hemangioma Associated with Hypoplastic Left Heart Syndrome Presenting as Sudden Infant Death Syndrome.
abstract: Primary cardiac tumors are rare in children with a low incidence varying from 0.0017 to 0.28% in autopsy studies. Approximately 90% of the reported primary cardiac tumors in the pediatric population are benign and the most common subtype is rhabdomyomas accounting for approximately 60%, while hemangiomas are rare primary tumors with a 5% incidence. Hypoplastic left heart syndrome is abnormal development of the left-sided cardiac structures, leading to obstruction of blood flow from the left ventricle out-flow tract. Here we report a case of tricuspid hemangioma in association with hypoplastic left heart syndrome, a rare association not previously reported in the literature.
authors.affiliation: Department of Pathology, Lady Hardinge Medical College, NEW DELHI, India.
authors.forename: Brijnandan
authors.initials: B
authors.lastname: Gupta
authors.forename: Shouriyo
authors.initials: S
authors.lastname: Ghosh
authors.forename: Maikal
authors.initials: M
authors.lastname: Kujur
authors.forename: Khushbu
authors.initials: K
authors.lastname: Khetan
authors.forename: Tarun
authors.initials: T
authors.lastname: Kumar
mesh_terms: D005260:Female; D006338:Heart Neoplasms / Q000150:complications / Q000175:diagnosis / Q000473:pathology*; D006392:Hemangioma, Cavernous / Q000150:complications / Q000175:diagnosis / Q000473:pathology*; D006801:Humans; D018636:Hypoplastic Left Heart Syndrome / Q000150:complications / Q000175:diagnosis / Q000473:pathology*; D007231:Infant, Newborn; D013398:Sudden Infant Death / Q000175:diagnosis / Q000209:etiology* / Q000473:pathology; D014261:Tricuspid Valve / Q000473:pathology