title: Primary Hepatic Amyloidosis Presenting as Acute-on-Chronic Liver Failure.
abstract: Systemic amyloidosis of amyloid light chain associated protein (AL), also called primary amyloidosis, frequently involves the liver, but rarely causes clinically apparent liver disease. The more common presentation is with acute renal failure. Hepatomegaly and mild elevation of alkaline phosphatase are the most common clinical and biochemical findings, respectively. We report a case of systemic amyloidosis of AL that clinically presented as acute-on-chronic liver failure and resulted in a fatal clinical course in a 56-year-old man.
authors.affiliation: Department of Hepatology, Institute of Liver and Biliary Sciences, Vasant Kunj, New Delhi, India.
authors.forename: Madhumita
authors.initials: M
authors.lastname: Premkumar
authors.affiliation: Department of Hepatology, Institute of Liver and Biliary Sciences, Vasant Kunj, New Delhi, India.
authors.forename: Devaraja
authors.initials: D
authors.lastname: Rangegowda
authors.affiliation: Department of Hepatology, Institute of Liver and Biliary Sciences, Vasant Kunj, New Delhi, India.
authors.forename: Tanmay
authors.initials: T
authors.lastname: Vyas
authors.affiliation: Department of Hepatology, Institute of Liver and Biliary Sciences, Vasant Kunj, New Delhi, India.
authors.forename: Anand
authors.initials: A
authors.lastname: Kulkarni
authors.affiliation: Department of Pathology, Institute of Liver and Biliary Sciences, Vasant Kunj, New Delhi, India.
authors.forename: Shrruti
authors.initials: S
authors.lastname: Grover
authors.affiliation: Department of Hepatology, Institute of Liver and Biliary Sciences, Vasant Kunj, New Delhi, India.
authors.forename: Rakhi
authors.initials: R
authors.lastname: Mahiwall
authors.affiliation: Department of Hepatology, Institute of Liver and Biliary Sciences, Vasant Kunj, New Delhi, India.
authors.forename: Shiv Kumar
authors.initials: SK
authors.lastname: Sarin