title: Functional near-tricuspid atresia in a patient with absent pulmonary valve and an intact ventricular septum.
abstract: Absent pulmonary valve with an intact ventricular septum is a rare malformation. We report a case of absent pulmonary valve and intact ventricular septum with functional near-tricuspid atresia caused by pulmonary regurgitation. Initial palliation with main pulmonary artery ligation and bilateral pulmonary artery banding was performed at 1 day of age. More antegrade flow across the tricuspid valve was recognised postoperatively, resulting in a successful right ventricular outflow tract reconstruction by a hand-sewn bileaflet polytetrafluoroethylene valve and modified Blalock-Taussig shunt at 11 days of age.
authors.affiliation: 1Department of Cardiology,Kobe Children's Hospital,Hyogo,Japan.
authors.forename: Yasunobu
authors.initials: Y
authors.lastname: Miki
authors.affiliation: 1Department of Cardiology,Kobe Children's Hospital,Hyogo,Japan.
authors.forename: Toshikatsu
authors.initials: T
authors.lastname: Tanaka
authors.affiliation: 2Department of Cardiovascular Surgery,Kobe Children's Hospital,Hyogo,Japan.
authors.forename: Yoshihiro
authors.initials: Y
authors.lastname: Oshima
mesh_terms: D000015:Abnormalities, Multiple; D006328:Cardiac Catheterization; D006348:Cardiac Surgical Procedures / Q000379:methods*; D003937:Diagnosis, Differential; D004452:Echocardiography; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D011664:Pulmonary Valve / Q000002:abnormalities* / Q000601:surgery; D011665:Pulmonary Valve Insufficiency / Q000175:diagnosis* / Q000601:surgery; D013902:Radiography, Thoracic; D018785:Tricuspid Atresia / Q000175:diagnosis* / Q000601:surgery; D054088:Ventricular Septum / Q000000981:diagnostic imaging*
keywords: Absent pulmonary valve; functional near-tricuspid atresia; intact ventricular septum