title: Steatocystoma multiplex suppurativa: case report of a rare condition.
abstract: Steatocystoma multiplex is a rare genetic disorder characterized by the presence of hamartomatous malformations at the junction of the pilosebaceous duct. It consists of encapsulated cystic lesions in the dermis, with adjacent sebaceous gland. When associated with inflammation, resembling hidradenitis, it is called steatocystoma multiplex suppurativa, a condition rarely reported. This is the first case of steatocystoma multiplex suppurativa reported in the Brazilian literature. Female patient, 23 years old, with papular and nodular cystic lesions that started in the armpits and groin, later spreading to the trunk, lower limbs, anticubital fossa, face and scalp. The presence of papular-nodular lesions associated with disseminated hidradenitis-like lesions in flexural areas and the histopathological diagnosis of steatocystoma defined the diagnosis of steatocystoma multiplex suppurativa.
authors.affiliation: Universidade do Estado do Rio de Janeiro (UERJ) - Rio de Janeiro (RJ), Brazil.
authors.forename: Cândida Naira Lima E Lima
authors.initials: CN
authors.lastname: Santana
authors.affiliation: Universidade do Estado do Rio de Janeiro (UERJ) - Rio de Janeiro (RJ), Brazil.
authors.forename: Daniele do Nascimento
authors.initials: DD
authors.lastname: Pereira
authors.affiliation: Universidade do Estado do Rio de Janeiro (UERJ) - Rio de Janeiro (RJ), Brazil.
authors.forename: Alice Paixão
authors.initials: AP
authors.lastname: Lisboa
authors.affiliation: Universidade do Estado do Rio de Janeiro (UERJ) - Rio de Janeiro (RJ), Brazil.
authors.forename: Juliana Martins
authors.initials: JM
authors.lastname: Leal
authors.affiliation: Universidade do Estado do Rio de Janeiro (UERJ) - Rio de Janeiro (RJ), Brazil.|Hospital Central do Exército (HCE) - Rio de Janeiro (RJ), Brazil.|Universidade do Grande Rio (Unigranrio) - Rio de Janeiro (RJ), Brazil.
authors.forename: Daniel Lago
authors.initials: DL
authors.lastname: Obadia
authors.affiliation: Universidade do Estado do Rio de Janeiro (UERJ) - Rio de Janeiro (RJ), Brazil.
authors.forename: Roberto Souto da
authors.initials: RS
authors.lastname: Silva
mesh_terms: D001706:Biopsy; D003937:Diagnosis, Differential; D004814:Epidermal Cyst / Q000473:pathology; D005260:Female; D017497:Hidradenitis Suppurativa / Q000473:pathology; D006801:Humans; D035583:Rare Diseases / Q000473:pathology; D012627:Sebaceous Glands / Q000473:pathology; D062685:Steatocystoma Multiplex / Q000473:pathology*; D013492:Suppuration; D055815:Young Adult