title: [Bullous Sweet's syndrome with pulmonary involvement].
abstract: Acute febrile neutrophilic dermatosis (Sweet's syndrome) is a rare dermatosis characterized by painful papules and plaques accompanied by cutaneous infiltration with neutrophilic granulocytes. Bullous changes are observed in some cases. We report about a patient with osteomyelofibrosis who developed fever accompanied by painful plaques and confluent papules on both arms and thighs. The course of the disease was complicated by blistering and pulmonary infiltrates. After the diagnosis of bullous Sweet's syndrome was established, systemic therapy with glucocorticoids was successful in treating skin lesions and dyspnea.
authors.affiliation: Abteilung für Dermatologie und Venerologie, Krankenanstalt Rudolfstiftung , Juchgasse 25, 1030, Wien, Österreich.
authors.forename: A
authors.initials: A
authors.lastname: Sesti
authors.affiliation: Abteilung für Dermatologie und Venerologie, Krankenanstalt Rudolfstiftung , Juchgasse 25, 1030, Wien, Österreich.|School of Medicine, Sigmund Freud University, Freudplatz 1, 1020, Wien, Österreich.
authors.forename: K
authors.initials: K
authors.lastname: Rappersberger
authors.affiliation: Abteilung für Dermatologie und Venerologie, Krankenanstalt Rudolfstiftung , Juchgasse 25, 1030, Wien, Österreich. Cposch81@gmail.com.|School of Medicine, Sigmund Freud University, Freudplatz 1, 1020, Wien, Österreich. Cposch81@gmail.com.|Children's Cancer Research Institute, Leukemia Biology Group, Zimmermannplatz 10, 1090, Wien, Österreich. Cposch81@gmail.com.
authors.forename: C
authors.initials: C
authors.lastname: Posch
mesh_terms: D000368:Aged; D001706:Biopsy; D001848:Bone Diseases, Developmental / Q000175:diagnosis / Q000188:drug therapy / Q000473:pathology; D003131:Combined Modality Therapy; D003937:Diagnosis, Differential; D017707:Erythrocyte Transfusion; D005938:Glucocorticoids / Q000627:therapeutic use; D016179:Granulocyte Colony-Stimulating Factor / Q000627:therapeutic use; D006801:Humans; D008171:Lung Diseases / Q000175:diagnosis* / Q000188:drug therapy / Q000473:pathology; D008297:Male; D009570:Nitriles; D055728:Primary Myelofibrosis / Q000175:diagnosis / Q000188:drug therapy / Q000473:pathology; D011720:Pyrazoles / Q000627:therapeutic use; D011743:Pyrimidines; D012867:Skin / Q000473:pathology; D012872:Skin Diseases, Vesiculobullous / Q000175:diagnosis* / Q000188:drug therapy / Q000473:pathology; D016463:Sweet Syndrome / Q000175:diagnosis* / Q000188:drug therapy / Q000473:pathology
chemical_list: D005938:Glucocorticoids; D009570:Nitriles; D011720:Pyrazoles; D011743:Pyrimidines; D016179:Granulocyte Colony-Stimulating Factor; C540383:ruxolitinib
keywords: Dermatoses; Extracutaneous manifestation; Glucocorticoids; Lung; Osteomyelofibrosis