title: Anaesthetic Management in a Child with Goldenhar Syndrome.
abstract: Goldenhar syndrome is a congenital disorder involving deformities of the face. It usually affects one side of the face only and poses significant challenges in the airway management. We herein, report an 8-year boy, known case of Goldenhar syndrome, who presented to our radiology suite for a magnetic resonance imaging (MRI) brain, followed by a computed tomography (CT) scan brain. The boy had various features of Goldenhar syndrome, e.g. cleft palate, absent right eye and ear, right mandibular hypoplasia, micrognathia, and preauricular tags. His developmental milestones were delayed. Airway evaluation showed Mallampati class II with limited movements of head and neck, which suggested possibility of difficult laryngoscopy and intubation. He had no vertebral anomalies or cardiac disease. A difficult airway continues to be a major cause of anaesthesia-related morbidity and mortality; and maintaining spontaneous breathing remains a vital technique in its management. Lack of anaesthesia-related complications with supraglottic devices encouraged us to present the advantage of utilising a laryngeal mask airway (LMA) under anaesthesia for successful management of predicted difficult airway.
authors.affiliation: Department of Anaesthesia, The Aga Khan University Hospital, Karachi.
authors.forename: Waqas Ahmed
authors.initials: WA
authors.lastname: Khan
authors.affiliation: Department of Anaesthesia, The Aga Khan University Hospital, Karachi.
authors.forename: Bushra
authors.initials: B
authors.lastname: Salim
authors.affiliation: Department of Anaesthesia, The Aga Khan University Hospital, Karachi.
authors.forename: Ausaf Ahmed
authors.initials: AA
authors.lastname: Khan
authors.affiliation: Department of Anaesthesia, The Aga Khan University Hospital, Karachi.
authors.forename: Shakaib
authors.initials: S
authors.lastname: Chughtai
mesh_terms: D058109:Airway Management; D000777:Anesthetics / Q000627:therapeutic use*; D002648:Child; D006053:Goldenhar Syndrome / Q000150:complications* / Q000000981:diagnostic imaging*; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D014057:Tomography, X-Ray Computed
chemical_list: D000777:Anesthetics