[Biliary atresia - signs and symptoms, diagnosis, clinical management].
Biliary atresia is a chronic cholangiopathy leading to progressive fibrosis of both intra- and extrahepatic bile ducts. The cause of the condition is unknown. Fundamental management of biliary atresia is surgical intervention and the outcomes of the treatment depend on the child's age with best results when performed within the first 2 months of life. Thus, the main role of pediatric healthcare is an urgent differential diagnosis and prompt qualification for the surgery, optimal postoperative management and early qualification for the liver transplantation in patients with persistent cholestasis. The authors discuss the clinical presentation, diagnosis and management of biliary atresia.
Klinika Gastroenterologii, Hepatologii, Zaburzeń Odżywiania I Pediatrii Instytut Pomnik Centrum Zdrowia Dziecka, Warszawa, Polska.
Ewa
E
Orłowska
Klinika Gastroenterologii, Hepatologii, Zaburzeń Odżywiania I Pediatrii Instytut Pomnik Centrum Zdrowia Dziecka, Warszawa, Polska.
Piotr
P
Czubkowski
Klinika Gastroenterologii, Hepatologii, Zaburzeń Odżywiania I Pediatrii Instytut Pomnik Centrum Zdrowia Dziecka, Warszawa, Polska.
Piotr
P
Socha
D001656:Biliary Atresia / Q000175:diagnosis / Q000178:diet therapy / Q000473:pathology* / Q000628:therapy; D003937:Diagnosis, Differential; D019468:Disease Management; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D016031:Liver Transplantation
 Kasai procedure;  children ; cholestasis