title: Hepatic perivascular epithelioid tumor (PEComa). A case report.
abstract: A 37-year-old female had liver nodules found in an abdominal ultrasound scan. The radiological features were suggestive of hepatocellular adenomas, although there were some atypical findings. Two years later, one of the nodules showed dimensional progression and intralesional hemorrhage. The patient underwent a left hepatectomy and the postoperative course was uneventful. The histological exam and the immunohistochemistry were consistent with the diagnosis of PEComa. The PEComa is a mesenchymal tumor rarely described in the liver. The preoperative diagnosis of PEComa is very difficult and, with this report, the authors intend to increase the limited knowledge relating to natural history and optimal treatment of this rare condition.
authors.affiliation: Gastroenterology Department, Centro Hospitalar São João, Faculty of Medicine of the University of Porto, Alameda Professor Hernâni Monteiro, 4200-319 Porto, Portugal.
authors.forename: Hélder
authors.initials: H
authors.lastname: Cardoso
authors.affiliation: Gastroenterology Department, Centro Hospitalar São João, Faculty of Medicine of the University of Porto, Alameda Professor Hernâni Monteiro, 4200-319 Porto, Portugal. Electronic address: hcmail@sapo.pt.
authors.forename: Marco
authors.initials: M
authors.lastname: Silva
authors.affiliation: Gastroenterology Department, Centro Hospitalar São João, Faculty of Medicine of the University of Porto, Alameda Professor Hernâni Monteiro, 4200-319 Porto, Portugal.
authors.forename: Filipe
authors.initials: F
authors.lastname: Vilas-Boas
authors.affiliation: Imagiology Department, Centro Hospitalar São João, Faculty of Medicine of the University of Porto, Porto, Portugal.
authors.forename: Rui
authors.initials: R
authors.lastname: Cunha
authors.affiliation: Pathology Department, Centro Hospitalar São João, Faculty of Medicine of the University of Porto, Porto, Portugal.
authors.forename: Joanne
authors.initials: J
authors.lastname: Lopes
authors.affiliation: General Surgery Department, Centro Hospitalar São João, Faculty of Medicine of the University of Porto, Porto, Portugal.
authors.forename: José Costa
authors.initials: JC
authors.lastname: Maia
authors.affiliation: Gastroenterology Department, Centro Hospitalar São João, Faculty of Medicine of the University of Porto, Alameda Professor Hernâni Monteiro, 4200-319 Porto, Portugal.
authors.forename: Guilherme
authors.initials: G
authors.lastname: Macedo
mesh_terms: D000328:Adult; D005260:Female; D006801:Humans; D008113:Liver Neoplasms / Q000175:diagnosis / Q000601:surgery; D054973:Perivascular Epithelioid Cell Neoplasms / Q000175:diagnosis / Q000601:surgery