title: Arrhythmogenic right ventricular cardiomyopathy with biventricular involvement and heart failure in a 9-year old girl.
abstract: Arrhythmogenic right ventricular cardiomyopathy (ARVC) is seldom recognized clinically in infancy or under the age of 10. We report a case of a 9-year-old girl with ARVC, who presented with signs and symptoms of heart failure and palpitations. Holter monitoring showed frequent premature ventricular beats and echocardiogram revealed dilated and dysfunctional right ventricle with normal tricuspid valve and no evidence of intracardiac shunt. Cardiac magnetic resonance showed classical features of ARVC with both ventricular involvements. After optimization of medical treatment the patient was referred for ICD implantation.
authors.affiliation: Aga Khan University Hospital, Karachi, aPakistan.
authors.forename: Fateh Ali Tipoo
authors.initials: FA
authors.lastname: Sultan
authors.affiliation: Aga Khan University Hospital, Karachi, aPakistan.
authors.forename: Mehnaz Atiq
authors.initials: MA
authors.lastname: Ahmed
authors.affiliation: Flinders University, Adelaide, fAustralia.
authors.forename: Jamie
authors.initials: J
authors.lastname: Miller
authors.affiliation: Flinders University of South Australia, bAustralia; CIRG, South Australian Health and Medical Research Institute, cAustralia; Cardiac Imaging, Southern Area Health Service, dAustralia; Department of Cardiovascular Medicine, Flinders Medical Centre, Flinders Drive, Bedford Park, Adelaide 5042, eAustralia.
authors.forename: Joseph B
authors.initials: JB
authors.lastname: Selvanayagam
keywords: ARVC; CMR; Dilated RV