title: Malignant Hepatic Epithelioid Hemangioendothelioma with Villaret Syndrome.
abstract: Malignant hepatic epithelioid hemangioendothelioma is a rare, vascular tumor of the liver with peak incidence in the middle age with a female preponderance and of unknown etiology. Majority of the tumors are asymptomatic. The gold standard for diagnosis of the tumor is liver histology showing presence of epithelioid tumor cells on a background of a hyaline stroma. Immunohistochemical positivity for CD31, CD34, Factor VIII, and Podoplanin (D2-40) is confirmatory. The treatment of choice is liver transplantation.
authors.affiliation: Institute of Liver Disease & Transplantation, Department of Pathology, Global Health City, Chennai, India.
authors.forename: Hanchanale
authors.initials: H
authors.lastname: Pavan
authors.affiliation: Institute of Liver Disease & Transplantation, Department of Pathology, Global Health City, Chennai, India.
authors.forename: Joy
authors.initials: J
authors.lastname: Varghese
authors.affiliation: Institute of Liver Disease & Transplantation, Department of Pathology, Global Health City, Chennai, India.
authors.forename: Kavya
authors.initials: K
authors.lastname: Harika
authors.affiliation: Institute of Liver Disease & Transplantation, Department of Pathology, Global Health City, Chennai, India.
authors.forename: Mukul
authors.initials: M
authors.lastname: Vij
authors.affiliation: Institute of Liver Disease & Transplantation, Department of Pathology, Global Health City, Chennai, India.
authors.forename: Venkataraman
authors.initials: V
authors.lastname: Jayanthi
authors.affiliation: Institute of Liver Disease & Transplantation, Department of Pathology, Global Health City, Chennai, India.
authors.forename: Mohamed
authors.initials: M
authors.lastname: Rela
keywords: CECT, contrast-enhanced computed tomography; EHE, epithelioid hemangioma; HEHE, hepatic epithelioid hemangioendothelioma; Villaret syndrome; epithelioid hemangioendothelioma; hepatic epethelioid hemangioendothelioma; malignant hepatic epitheliod hemangioendothelioma