title: Juvenile Hyaline Fibromatosis: A 10-year Follow-up.
abstract: Juvenile hyaline fibromatosis (JHF) is a rare hereditary disease with an autosomal recessive transmission. JHF is characterized by papulonodular skin lesions, osteolytic bone lesions, flexural joint contractures, and gingival hyperplasia and usually diagnosed in infancy or early childhood. JHF is thought to be a disorder of collagen metabolism and characterized by homogenous amorphous eosinophilic material and fibrous tissue. We report the case of a 14-year-old male child with multiple papulonodular skin lesions, progressive flexion contractures of joints, and severe gingival hyperplasia, with a 10-year follow-up. Although the lesions were totally removed thrice during the last 10 years, they recurred rigorously.
authors.affiliation: Department of Periodontology, Faculty of Dentistry, Karadeniz Technical University, Trabzon, Turkey.
authors.forename: Esra
authors.initials: E
authors.lastname: Baltacioglu
authors.affiliation: Department of Periodontology, Faculty of Dentistry, Kocaeli University, Kocaeli, Turkey.
authors.forename: Esra
authors.initials: E
authors.lastname: Guzeldemir
authors.affiliation: Department of Periodontology, Faculty of Dentistry, Karadeniz Technical University, Trabzon, Turkey.
authors.forename: Erkan
authors.initials: E
authors.lastname: Sukuroglu
authors.affiliation: Department of Pathology, Faculty of Medicine, Karadeniz Technical University, Trabzon, Turkey.
authors.forename: Kadriye
authors.initials: K
authors.lastname: Yildiz
authors.affiliation: Beytepe Hospital Dental Clinic, Hacettepe University, Ankara, Turkey.
authors.forename: Pinar
authors.initials: P
authors.lastname: Yuva
authors.affiliation: Department of Periodontology, Faculty of Dentistry, Karadeniz Technical University, Trabzon, Turkey.
authors.forename: Güven
authors.initials: G
authors.lastname: Aydin
authors.affiliation: Department of Plastic and Reconstructive Surgery, Faculty of Medicine, Karadeniz Technical University, Trabzon, Turkey.
authors.forename: Naci
authors.initials: N
authors.lastname: Karacal
keywords: Gingival hyperplasia; gingivectomy; juvenile hyaline fibromatosis