title: Deep Sedation Technique for Dental Rehabilitation of a Patient with Klippel-Feil Syndrome.
abstract: Klippel-Feil syndrome (KFS) is a congenital anomaly characterized by a defect in the formation or segmentation of the cervical vertebrae, resulting in their fusion. The clinical triad of the syndrome consists of short neck, low posterior hairline, and limited neck movement, although fewer than 50 percent of patients demonstrate all three clinical features. The short neck and its immobility and instability present a significant challenge for endotracheal intubation. The purpose of this paper is to describe the management of a 13-year-old patient with KFS, extensive dental caries, and restricted mouth opening using a deep sedation technique in the operating room, which allowed successful completion of dental treatment.
authors.affiliation: Pediatric dental resident, in the Department of Pediatric Dentistry, University of Florida College of Dentistry, Gainesville, Fla., USA;, Email: h_kabbos@hotmail.com.
authors.forename: Halima
authors.initials: H
authors.lastname: Abukabbos
authors.affiliation: Professor and Executive Vice-Chair, Chief, Division of Neuroanesthesia Department of Anesthesiology Sidney Kimmel Medical College, Thomas Jefferson University, Philadelphia, Pa., USA.
authors.forename: Michael
authors.initials: M
authors.lastname: Mahla
authors.affiliation: Clinical associate professor and program director, in the Department of Pediatric Dentistry, University of Florida College of Dentistry, Gainesville, Fla., USA.
authors.forename: Abi O
authors.initials: AO
authors.lastname: Adewumi
mesh_terms: D000293:Adolescent; D058109:Airway Management; D000768:Anesthesia, General; D054810:Deep Sedation / Q000379:methods*; D003730:Dental Care for Persons with Disabilities; D003731:Dental Caries / Q000534:rehabilitation* / Q000628:therapy*; D005146:Facial Asymmetry; D005260:Female; D006801:Humans; D007714:Klippel-Feil Syndrome / Q000150:complications* / Q000503:physiopathology; D008334:Mandible / Q000002:abnormalities; D008437:Maxilla / Q000002:abnormalities; D014103:Torticollis / Q000150:complications