title: An Unusual Presentation of Limited Granulomatosis with Polyangiitis Involving Vagina and Urethra.
abstract: Granulomatosis with polyangiitis (GPA) is a systemic necrotizing granulomatosis vasculitis characterized by predilection to affect small- and medium-sized blood vessels and commonly affects the upper and lower respiratory tract and kidneys in most cases. Genital involvement is reported in <1% of cases in large cohorts and nearly all cases have been in the setting of multisystemic disease or during the course of the disease in patients already diagnosed as GPA. A case is presented of uncommon limited urogenital GPA in a 66-year-old woman with an irregular mass occupying urethra and vagina. The patient showed a good response after Corticoids and Methotrexate.
authors.affiliation: Rheumatology Unit, Hospital General de Villarrobledo, Villarrobledo, Albacete, Spain.
authors.forename: Sandra
authors.identifier: 0000-0002-8263-0764
authors.initials: S
authors.lastname: Soro Marín
authors.affiliation: Department of Rheumatology, Complejo Hospitalario Universitario de Albacete, Albacete, Spain.
authors.forename: Enrique
authors.initials: E
authors.lastname: Júdez Navarro
authors.affiliation: Department of Rheumatology, Complejo Hospitalario Universitario de Albacete, Albacete, Spain.
authors.forename: Manuela
authors.initials: M
authors.lastname: Sianes Fernández
authors.affiliation: Department of Rheumatology, Complejo Hospitalario Universitario de Albacete, Albacete, Spain.
authors.forename: Ginés
authors.initials: G
authors.lastname: Sánchez Nievas
authors.affiliation: Department of Urology, Complejo Hospitalario Universitario de Albacete, Albacete, Spain.
authors.forename: Juan Gabriel Lorenzo
authors.initials: JG
authors.lastname: Romero