title: It's Rare So Be Aware: Pleuropulmonary Blastoma Mimicking Congenital Pulmonary Airway Malformation.
abstract: Pleuropulmonary blastoma (PPB) is a rare aggressive malignant tumor of infancy and early childhood. The tumor arises in the lung and pleura and is regarded as a pulmonary dysontogenetic or embryonic neoplasm. Four types are defined in literature. Type I PPB is a rare, cystic lung neoplasm in infants characterized by subtle malignant changes and a good prognosis. Recurrences after type I PPB are usually advanced with a poor prognosis. We report this case to increase awareness about this entity so that the pediatricians, pediatric surgeons, radiologist, and pathologist recognize it early.
authors.affiliation: Pediatric Surgery Unit, Department of Surgery, Salmaniya Medical Complex, Manama, Bahrain.
authors.forename: Fayza
authors.initials: F
authors.lastname: Haider
authors.affiliation: Pediatric Department, Salmaniya Medical Complex, Manama, Bahrain.
authors.forename: Khulood
authors.initials: K
authors.lastname: Al Saad
authors.affiliation: Department of Pathology, Salmaniya Medical Complex, Manama, Bahrain.
authors.forename: Fatima
authors.initials: F
authors.lastname: Al-Hashimi
authors.affiliation: Department of Radiology, Salmaniya Medical Complex, Manama, Bahrain.
authors.forename: Hakima
authors.initials: H
authors.lastname: Al-Hashimi
keywords: Pleuropulmonary Blastoma; airway (includes related subject matter); benign or congenital lesions; infant; lung; pediatric