title: Protein-losing enteropathy in biventricular circulation precipitated by mild stenosis of the inferior caval vein in conjunction with total occlusion of the superior caval vein: a word of caution.
abstract: We report the case of a young boy with a history of total occlusion of the superior caval vein, diagnosed early after complex neonatal cardiac surgery, who developed severe protein-losing enteropathy. Protein-losing enteropathy was precipitated by a relatively mild stenosis at the junction of the inferior caval vein with the right atrium. Percutaneous stent dilation of the veno-atrial junction definitively relieved the stenosis, and the protein-losing enteropathy subsequently resolved.
authors.affiliation: 1Department of Paediatric Cardiology,Ospedale Infantile Regina Margherita,Città della Salute e della Scienza,Turin,Italy.
authors.forename: Davide
authors.initials: D
authors.lastname: Marini
authors.affiliation: 3Department of Paediatric Cardiology,Royal Belfast Hospital for Sick Children,Belfast,Northern Ireland,UK.
authors.forename: Brian A
authors.initials: BA
authors.lastname: McCrossan
authors.affiliation: 1Department of Paediatric Cardiology,Ospedale Infantile Regina Margherita,Città della Salute e della Scienza,Turin,Italy.
authors.forename: Gabriella
authors.initials: G
authors.lastname: Agnoletti
mesh_terms: D002648:Child; D003251:Constriction, Pathologic / Q000000981:diagnostic imaging; D006801:Humans; D008297:Male; D011504:Protein-Losing Enteropathies / Q000209:etiology* / Q000503:physiopathology; D015607:Stents; D013479:Superior Vena Cava Syndrome / Q000150:complications* / Q000000981:diagnostic imaging* / Q000601:surgery; D014057:Tomography, X-Ray Computed
keywords: CT; Protein-losing enteropathy; systemic vein occlusion