title: Rapidly progressive IgA nephropathy.
abstract: A 14-year-old boy presented with macroscopic hematuria and a rapid deterioration in renal function. Percutaneous renal biopsy demonstrated severe crescentic IgA nephropathy (IgAN) with extensive (88%) glomerular crescent formation. After started intravenous administration of high-dose pulse methylprednisolone, severe nausea and general malaise accompanied by a rapid increase in Blood Urea Nitrogen (BUN) and serum creatinine levels appeared, however, the renal function ameliorated rapidly and fully revovered by following oral administration of corticosteroid. The clinical presentation of our case seems to be very remarkable compared to previously reported cases of rapidly progressive IgAN.
authors.affiliation: Department of Pediatric Cardiology and Nephrology, Kyoto Prefectural University of Medicine Graduate School of Medical Science, Kawaramachi-Hirokoji, Kamigyo-ku, 602-8566, Kyoto, Japan.
authors.forename: Naho
authors.initials: N
authors.lastname: Kobayashi
authors.affiliation: Department of Pediatric Cardiology and Nephrology, Kyoto Prefectural University of Medicine Graduate School of Medical Science, Kawaramachi-Hirokoji, Kamigyo-ku, 602-8566, Kyoto, Japan. mnishida@koto.kpu-m.ac.jp.
authors.forename: Masashi
authors.initials: M
authors.lastname: Nishida
authors.affiliation: Department of Pediatrics, Kyoto Prefectural University of Medicine Graduate School of Medical Science, Kyoto, Japan.
authors.forename: Michiko
authors.initials: M
authors.lastname: Aoyama
authors.affiliation: Department of Pediatrics, Kyoto Prefectural University of Medicine Graduate School of Medical Science, Kyoto, Japan.
authors.forename: Kentaro
authors.initials: K
authors.lastname: Yokoi
authors.affiliation: Department of Pediatric Cardiology and Nephrology, Kyoto Prefectural University of Medicine Graduate School of Medical Science, Kawaramachi-Hirokoji, Kamigyo-ku, 602-8566, Kyoto, Japan.
authors.forename: Tomoyo
authors.initials: T
authors.lastname: Yahata
authors.affiliation: Department of Pediatric Cardiology and Nephrology, Kyoto Prefectural University of Medicine Graduate School of Medical Science, Kawaramachi-Hirokoji, Kamigyo-ku, 602-8566, Kyoto, Japan.
authors.forename: Tatsujiro
authors.initials: T
authors.lastname: Oka
authors.affiliation: Department of Pediatric Cardiology and Nephrology, Kyoto Prefectural University of Medicine Graduate School of Medical Science, Kawaramachi-Hirokoji, Kamigyo-ku, 602-8566, Kyoto, Japan.
authors.forename: Koichi
authors.initials: K
authors.lastname: Sakata
authors.affiliation: Department of Pediatric Cardiology and Nephrology, Kyoto Prefectural University of Medicine Graduate School of Medical Science, Kawaramachi-Hirokoji, Kamigyo-ku, 602-8566, Kyoto, Japan.
authors.forename: Isao
authors.initials: I
authors.lastname: Shiraishi
authors.affiliation: Department of Pediatric Cardiology and Nephrology, Kyoto Prefectural University of Medicine Graduate School of Medical Science, Kawaramachi-Hirokoji, Kamigyo-ku, 602-8566, Kyoto, Japan.
authors.forename: Toshiyuki
authors.initials: T
authors.lastname: Itoi
authors.affiliation: Department of Pediatric Cardiology and Nephrology, Kyoto Prefectural University of Medicine Graduate School of Medical Science, Kawaramachi-Hirokoji, Kamigyo-ku, 602-8566, Kyoto, Japan.
authors.forename: Kenji
authors.initials: K
authors.lastname: Hamaoka
keywords: Acute renal failure; Diffuse crescentic glomerulonephritis; IgA nephropathy; Rapidly progressive glomerulonephritis